ANSD is typically identified at birth or in early childhood. In 2010, Berlin et al. [9] reported260 patients with ANSD: most cases occurred in the age stage under 24 months and accounted for33.84% of all cases; overall, patients aged 18 years and under comprised the majority of the population (88.08%). In the present study, UANSD was diagnosed in ages ranging from 0.8 to 18 years old. The age at onset was found to be from 0.5 to 9 years, and the average age at onset was 4.1 years. From the reported cases of UANSD, we also found that the majority of sufferers were in the childhood group.