On the basis of reported cases of UANSD and the 14 patients identified in the present study, the hearing loss in the ears diagnosed as exhibiting ANSD ranged from moderate to profound, and the majority of patients had severe or profound hearing loss. Patients with UANSD can present normal hearing level or sensorineural hearing loss of different degrees on the contralateral side. It can also be accompanied by peripheral neuropathy. However, to date, none of the patients have complained of dizziness。